Biologic Considerations
Ionizing radiation may interact with
individual cells via direct ionization of DNA or other critical molecules,
or indirectly by ionizing water molecules to form free radicals, which
themselves are freely diffusible and can damage chromosomal DNA or
critical membrane sites.
In
general, the radiation dose necessary to destroy the function of a
differentiated cell, such as a smooth muscle cell or endothelial cell, is
far greater than the dose of radiation necessary to prevent cell division.
Most lethally irradiated cells die during the mitotic process. It is
unclear what, if any, the relative contribution of apoptosis is to
postirradiation cell death seen in the arterial wall.
In radiotherapy of parenchymal organs, injury
to capillaries and arterioles of normal parenchyma accounts for the
majority of delayed effects of radiation. Experimental studies of large
arteries (greater than 100 µm in diameter) have revealed that these
vessels are less sensitive to radiation than smaller caliber vessels.
Rarely, arterial perforation may occur. Large veins appear to be even more
resistant to radiation than corresponding size arteries.
The risk of late coronary artery disease (CAD) as a consequence of radiation therapy has been best assessed in studies of patients irradiated for thoracic neoplasms. A retrospective analysis of Hodgkin's disease patients who received mediastinal radiation as part of their treatment reported a relative risk of myocardial infarction of 2.56 . Another retrospective study reported a relative hazard of death of 3.2 in patients who received high-dose radiation involving the heart for treatment of carcinoma of the left breast. Factors that were thought to be important in this increased mortality were the irradiated volume, radiation energy, fractionation (number and size of individual treatments), and total dose. Finally, a review of 2,232 Hodgkin's disease patients receiving mantel radiation reported the overall relative risk for cardiac death was 3.1 (confidence interval, 2.4 to 3.7). Mediastinal radiation of 30 Gy or less (n = 385 patients) did not increase risk; above 30 Gy (n = 1,830), relative risk was 3.5 (confidence interval, 2.7 to 4.3). Interestingly, the relative risk decreased as the age at the time of treatment increased. The latency for these events in the population was as long as 5 years. The risk of secondary neoplasms because of radiation of a small volume of tissue appears to be exceedingly low.
Late Effects
The administration of significant doses of
therapeutic radiation has been associated with a vasculopathy, which
affects vessels in the radiated region. In parenchymal organ radiation,
the principal effect of radiation injury to blood vessels is at the
level of the capillaries and arterioles. The effects on large arteries,
such as the epicardial coronary arteries, analyzed in retrospective
studies of patients who have received radiation for thoracic neoplasms,
appear to be dose-related and
inversely related to the age of the patient at the time of irradiation.
The earliest evidence of coronary disease appears 5 years after
radiation. These data are derived from studies of patients who
have received fractionated doses of radiation and have had the entire
heart in the radiated field. The long-term effects of single-dose (as
opposed to fractionated dose) radiation of the magnitude suggested by
the animal trials are not known.
It is clear, however, that the risk of late complication, such as
myocardial infarction or pericarditis, is related to the volume of
radiated tissue. The late risk of radiation to the arterial wall
is thus minimized when the volume of treated tissue is small, as with
treatment by endovascular sources.
Radiation Injury
The heart was thought to be resistant to
radiation injury in the first half of the twentieth century. High-dose
radiation was delivered without proper cardiac shielding. Many reports of
radiation-induced cardiac abnormalities changed the perception of safety
of radiation to the heart. Radiation, when used in the treatment of
mediastinal tumors, primarily Hodgkin's and nonHodgkin's lymphoma, and
spinal irradiation can cause cardiac abnormality in as many as 40% of
patients. This awareness and the availability of better radiation
techniques in the last decade have led to careful use of high-dose
radiation to the chest with proper cardiac shielding. More than 30 Gy to
the chest is usually not used. Therefore, the long-term effects of modern
radiation may be less severe than before. However, due to better long-term
survival of patients who received radiation in the past and delayed
manifestation of cardiac effects, we are likely to continue to encounter
these problems. The injuries due to radiation involve various cardiac
structures and can cause acute or delayed manifestations.
Pericardium
Acute pericarditis due to radiation is rare (approximately 2% of
total population undergoing chest radiation). Over the years,
approximately one-half of the patients develop echocardiographically
demonstrable abnormalities, and approximately 5% develop clinically
significant pericardial disease.
Myocardium
Radiation causes progressive fibrin
deposition and capillary destruction, leading to fibrosis in the
myocardium . This leads to mild left ventricular dysfunction not
requiring specific treatment. Coronary artery disease should be
ruled out when significant systolic dysfunction of the left ventricle is
identified. Restrictive cardiomyopathy has also been described from
radiation treatment
Valves
Valvular thickening is present in many
patients after radiation treatment, but significant valvular disease is
an infrequent sequela. The mean time from radiation to clinically
recognizable valvular disease is approximately 10 years, and the
symptoms develop approximately 5 years after that. Aortic and mitral
replacement from radiation-induced sclerosis with significant aortic
stenosis or mitral regurgitation has been reported. Pulmonary and
tricuspid valve disease is even less common
Conduction System
Nodal and infranodal conduction
abnormalities occur with radiation injury. Although right bundle branch
block is most common, complete heart block has been reported. Management
of these abnormalities is similar to that from other causes.
Coronary Arteries
External radiation injury involves the
proximal portion of coronary arteries. Left and right coronary ostia and
proximal left anterior descending and left circumflex are involved in
most cases. The lesions have an increased number of plasma cells with
paucity of lipids. Large, bizarre fibroblasts are also present. Coronary
disease commonly presents approximately 5 years after radiation but can
present as late as 29 years. Predisposing factors other than the total
dose of radiation are not clearly identified. Patients can present with
any ischemic complication, such as angina, MI, arrhythmia, or heart
failure. Children treated with chest radiation have a higher risk of MI.
For significant left main stenosis, coronary artery bypass grafting with
left internal mammary artery conduit is recommended, although surgery
can be technically difficult due to excessive scarring. For other focal
lesions, percutaneous transluminal coronary angioplasty can be useful.
Intracoronary radiation is now used to treat recurring in-stent
restenosis. The long-term effects of this type of therapy remain
unknown.
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